Mitochondrial creatine sensitivity is lost in the D2.mdx model of Duchenne muscular dystrophy and rescued by the mitochondrial-enhancing compound Olesoxime.
Bellissimo CA, Delfinis LJ, Hughes MC, Turnbull PC, Gandhi S, DiBenedetto SN, Rahman FA, Tadi P, Amaral CA, Dehghani A, Cobley JN, Quadrilatero J, Schlattner U, Perry CGR.
Bellissimo CA, et al. Among authors: rahman fa.
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PMID: 36689672
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