Nerve cell lesions caused by 3-hydroxyglutaric acid: a possible mechanism for neurodegeneration in glutaric acidaemia I

J Inherit Metab Dis. 1997 Jul;20(3):387-90. doi: 10.1023/a:1005342331229.
No abstract available

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adenosine Triphosphate / metabolism
  • Amino Acid Metabolism, Inborn Errors / metabolism*
  • Animals
  • Electrophysiology
  • Glutarates / blood*
  • Glutarates / toxicity*
  • Hippocampus / cytology
  • Hippocampus / drug effects
  • Nerve Degeneration / physiopathology*
  • Nervous System Diseases / metabolism*
  • Neurons / drug effects*
  • Organ Culture Techniques
  • Rats

Substances

  • 3-hydroxyglutaric acid
  • Glutarates
  • glutaconic acid
  • Adenosine Triphosphate
  • glutaric acid