The authors report two cases of renal cell carcinoma in children. A tumor occurring in a eight-year-old girl was composed of granular and oncocytic cells with obvious nuclear atypia. The other renal neoplasm, occurring in a nine-year-old boy, had a papillary pattern and was composed of small cells with mild nuclear atypia. In both patients, the tumor was confined to the kidney; radical nephrectomy was performed and patients were free of disease-with a follow-up of four years and one year, respectively.