Angiosarcoma metastatic to the orbit

Arch Ophthalmol. 1996 Jan;114(1):93-6. doi: 10.1001/archopht.1996.01100130089017.

Abstract

Angiosarcoma is a rare malignant endothelial cell tumor. Few reports of primary orbital angiosarcoma exist in the literature. A 46-year-old woman had a 3-month history of progressive diplopia and right-sided exophthalmos. Magnetic resonance imaging showed a right intraconal mass, consistent with a cavernous hemangioma. Ultrasound examination showed a isolated mass with moderate vascularity, consistent with a metastatic lesion. Subtotal excision through a lateral orbitotomy was performed. Tissue was stained with hematoxylineosin, periodic acid-Schiff, and immunohistochemical stains for factor-VIII-related antigen and Ulex europaeus agglutinin I lectin. Lateral orbitotomy biopsy specimens showed an angiosarcoma, similar to a primary breast angiosarcoma that had been resected 2 years previously. The patient initially underwent orbital exenteration for her only known metastasis. Despite a multidisciplinary and aggressive approach to this tumor, the tumor recurred, and the patient died.

Publication types

  • Case Reports

MeSH terms

  • Breast Neoplasms / pathology*
  • Breast Neoplasms / surgery
  • Chemotherapy, Adjuvant
  • Diplopia / diagnosis
  • Exophthalmos / diagnosis
  • Female
  • Hemangiosarcoma / diagnosis
  • Hemangiosarcoma / secondary*
  • Hemangiosarcoma / therapy
  • Humans
  • Magnetic Resonance Imaging
  • Mastectomy, Radical
  • Middle Aged
  • Neoplasm Recurrence, Local
  • Orbital Neoplasms / diagnosis
  • Orbital Neoplasms / secondary*
  • Orbital Neoplasms / therapy
  • Radiotherapy, Adjuvant
  • Tomography, X-Ray Computed