Glycan microheterogeneity of alpha 1-antitrypsin in serum and meconium from normal and cystic fibrosis patients by crossed immunoaffinoelectrophoresis with different lectins (Con A, LCA, WGA)

Clin Chim Acta. 1993 Jun 16;215(2):173-87. doi: 10.1016/0009-8981(93)90124-m.

Abstract

In order to test whether abnormalities of glycosylation occur in cystic fibrosis (CF), the glycan microheterogeneity of alpha 1-antitrypsin (alpha 1-AT) was studied in serum and meconium from normal individuals and patients with cystic fibrosis, by crossed immunoaffinoelectrophoresis (CIAE) using free Concanavalin A (Con A), Lens culinaris lectin (LCA) and wheat germ agglutinin (WGA). Three main results emerged from this study: (1) modification of glycosylation in serum alpha 1-AT from patients with cystic fibrosis were only significant with free Con A and WGA; this probably results from a reduced synthesis of the bi-antennary side-chains or by their increased catabolism. (2) Differences in isoforms found in alpha 1-AT from normal individuals and patients with CF using free Con A, LCA, were more pronounced in the meconium than in the serum; this may provide a useful test in diagnosis of cystic fibrosis. (3) There was parallelism between the behaviour of alpha 1-AT in serum and meconium from patients with CF using LCA, Con A; this may be explained by different types or levels of disfunction affecting a glycosylation mechanism.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adult
  • Concanavalin A
  • Cystic Fibrosis / metabolism*
  • Glycosylation
  • Humans
  • Immunoelectrophoresis, Two-Dimensional / methods*
  • Infant, Newborn
  • Lectins*
  • Meconium / chemistry*
  • Plant Lectins*
  • Polysaccharides / analysis
  • Polysaccharides / metabolism*
  • Wheat Germ Agglutinins
  • alpha 1-Antitrypsin / analysis
  • alpha 1-Antitrypsin / metabolism*

Substances

  • Lectins
  • Plant Lectins
  • Polysaccharides
  • Wheat Germ Agglutinins
  • alpha 1-Antitrypsin
  • lentil lectin
  • Concanavalin A