Eight years after removal of an adenoid cystic carcinoma (ACC = cylindroma) of the parotid gland, a female patient of 41 years of age developed isolated multiple lung metastases. She died three years later in the course of a respiratory insufficiency. Basing on this typical case record, the very rare ACC is presented, which has a tendency to pulmonary metastasising. The pathology, course of the disease, treatment and indication for performing a lung transplant in similar cases are discussed.