[Abnormalities in regulation system of granulopoiesis]

Rinsho Ketsueki. 1993 May;34(5):557-61.
[Article in Japanese]

Abstract

We studied the effects of several cytokines on the development of granulocyte-macrophage (GM) progenitors using the serum-deprived culture. SCF plays an important role in the GM-CSF- or IL-3-dependent production of neutrophils and macrophages. In vitro colony assay also suggests an increase in sensitivity of GM progenitors to cytokines (GM-CSF, IL-3, G-CSF and/or SCF) in a patient with juvenile chronic myelogenous leukemia. A high level of serum IFN-gamma was associated with leukopenia and thrombocytopenia in a patient with hemophagocytic syndrome. Based on the evidence that IFN-gamma significantly inhibited the proliferation of GM progenitors, IFN-gamma-mediated suppression was suggested as one of the mechanisms causing cytopenia. In patients with aplastic anemia and neutropenia, an increase of serum G-CSF levels was observed when neutrophils decreased remarkably in number. However, the serum SCF levels were constant in these patients. A failure of SCF to enhance colony growth in some patients with aplastic anemia implies qualitative abnormalities of hematopoietic progenitors.

Publication types

  • English Abstract

MeSH terms

  • Anemia, Aplastic / physiopathology
  • Cells, Cultured
  • Cytokines / physiology*
  • Granulocytes / physiology*
  • Hematopoiesis / physiology*
  • Hematopoietic Cell Growth Factors / physiology
  • Humans
  • Leukemia, Myelogenous, Chronic, BCR-ABL Positive / physiopathology
  • Neutropenia / physiopathology
  • Stem Cell Factor

Substances

  • Cytokines
  • Hematopoietic Cell Growth Factors
  • Stem Cell Factor