Platelets with 10% of the normal amount of glycoprotein VI have an impaired response to collagen that results in a mild bleeding tendency

Br J Haematol. 1995 Jan;89(1):124-30. doi: 10.1111/j.1365-2141.1995.tb08900.x.

Abstract

Platelet glycoprotein VI (GPVI), a 62kD membrane protein, has been identified as one of the platelet receptors for collagen, since GPVI-deficient platelets exhibit abnormal responses to collagen and an abnormal bleeding tendency. We report a female patient with a mild bleeding history whose platelets expressed 10% GPVI of normal platelets. Shape change, aggregation and ATP release of the patient's platelets were completely absent in response to 1-5 micrograms/ml collagen but present normally in response to ADP and Ca2+ ionophore A23187. Adhesion of the patient's platelets to coated collagen was mildly affected (40-60% of normal platelets) in spite of only 10% expression of GPVI. Flow cytometrical studies revealed that the patient's platelets expressed normal amounts of the GPIa/IIa complex. These results suggest that platelet GPVI is less involved in adhesion to collagen than shape change and aggregation induced by collagen.

Publication types

  • Case Reports
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adenosine Diphosphate / pharmacology
  • Adenosine Triphosphate / blood
  • Antigens, CD / blood
  • Blood Platelets / chemistry*
  • Blood Platelets / drug effects
  • Blood Platelets / pathology
  • CD36 Antigens
  • Calcimycin / pharmacology
  • Cell Adhesion / physiology
  • Cells, Cultured
  • Collagen / metabolism
  • Collagen / pharmacology*
  • Female
  • Hemorrhagic Disorders / blood*
  • Humans
  • Immunoblotting
  • Middle Aged
  • Platelet Aggregation / drug effects*
  • Platelet Membrane Glycoproteins / analysis
  • Thrombasthenia / blood

Substances

  • Antigens, CD
  • CD36 Antigens
  • Platelet Membrane Glycoproteins
  • Calcimycin
  • Adenosine Diphosphate
  • Adenosine Triphosphate
  • Collagen