Altered muscle saccharide pattern in X-linked muscular dystrophy

Arch Neurol. 1984 Jan;41(1):39-42. doi: 10.1001/archneur.1984.04050130045020.

Abstract

Five lectins were used as fluorescence microscopic markers for sugar residues in skeletal muscle. Biopsy specimens were taken from patients with X-linked muscular dystrophy (Duchenne's and Becker's), patients with other neuromuscular diseases, and normal controls. In both the controls and the pathologic samples, concanavalin A gave a bright fluorescence of the myofiber surface, whereas soybean agglutinin and Dolichos biflorus agglutinin fluorescence was negative. Peanut agglutinin and wheat germ agglutinin were more avidly bound to the sarcolemma and/or endomysial connective tissue in the patients with X-linked muscular dystrophy than in the controls or the patients with other conditions. The altered saccharide pattern may reflect either a myofiber membrane change or a specific mesenchymal reaction in the dystrophic muscle.

MeSH terms

  • Adolescent
  • Adult
  • Aged
  • Carbohydrate Metabolism*
  • Child
  • Child, Preschool
  • Female
  • Genetic Linkage
  • Humans
  • Lectins / metabolism
  • Male
  • Microscopy, Fluorescence
  • Middle Aged
  • Muscles / metabolism*
  • Muscles / pathology
  • Muscular Dystrophies / genetics
  • Muscular Dystrophies / metabolism*
  • Muscular Dystrophies / pathology
  • Neuromuscular Diseases / metabolism
  • Neuromuscular Diseases / pathology
  • X Chromosome

Substances

  • Lectins