Vitreous fluorophotometry in congenital stationary nightblindness

Arch Ophthalmol. 1983 Apr;101(4):574-6. doi: 10.1001/archopht.1983.01040010574008.

Abstract

Vitreous fluorophotometry was performed on eyes with three kinds of congenital stationary nightblindness: Oguchi's disease (two cases), X-linked congenital stationary nightblindness (two cases), and fundus albipunctatus (one case). The results were compared with the electroretinogram (ERG) and the electro-oculogram (EOG). In spite of the variable degree of abnormality of the ERG and EOG, all eyes showed normal values on vitreous fluorophotometry. These results strongly suggest that the blood-retinal barrier in congenital stationary nightblindness is intact and that the electrophysiological results and the functioning of the blood-retinal barrier do not correlate in these diseases.

Publication types

  • Case Reports

MeSH terms

  • Adolescent
  • Adult
  • Dark Adaptation
  • Diagnosis, Differential
  • Electrooculography
  • Electroretinography
  • Female
  • Fluorescein Angiography
  • Genetic Linkage
  • Humans
  • Male
  • Night Blindness / congenital*
  • Night Blindness / diagnosis
  • Night Blindness / genetics
  • Photometry
  • Visual Acuity
  • X Chromosome