Hemiconvulsion-hemiplegia-epilepsy syndrome is a rare and severe neurological condition that results from prolonged status epilepticus in infancy and early childhood. This syndrome is characterized by unilateral prolonged seizures, primarily clonic in nature, which are followed by transient or permanent ipsilateral hemiplegia. In this report, we present the case of a 3-year-old girl who exhibited persistent left hemiparesis after experiencing an episode of prolonged focal seizures at the age of 2 years. Comprehensive neurological evaluation and brain MRI conducted in our department confirmed the diagnosis of hemiconvulsion-hemiplegia-epilepsy syndrome in its chronic phase.
Keywords: Epilepsy; Hemiconvulsion; Hemiplegia; MRI; Status epilepticus.
© 2024 The Authors. Published by Elsevier Inc. on behalf of University of Washington.