We present the cases of 2 children diagnosed with extrahepatic portosystemic shunts, a very rare vascular anomaly, on investigation of cardiac symptomatology. Poorly developed portal venous systems necessitated staged shunt occlusion. This was achieved using atrial flow regulator devices positioned in an inferior vena cava stent platform performed in the cardiac catheterization laboratory.
Keywords: atrial flow regulator; atrial flow restrictor; inferior vena cava stent; portosystemic shunt; pulmonary hypertension.
© 2024 The Authors.