Abstract
Spiradenocarcinomas are rare malignant skin adnexal tumors. We describe a novel case of a patient with an aggressive CDKN2A-mutated spiradenocarcinoma who responded to a CDK4/6 inhibitor. This case highlights the unique nature of spiradenocarcinomas as well as the potential benefit of targeted therapy.
MeSH terms
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Adenocarcinoma / drug therapy
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Adenocarcinoma / genetics
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Adenocarcinoma / pathology
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Cyclin-Dependent Kinase 4 / genetics
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Cyclin-Dependent Kinase 6 / antagonists & inhibitors
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Cyclin-Dependent Kinase 6 / genetics
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Cyclin-Dependent Kinase Inhibitor p16* / genetics
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Female
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Humans
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Male
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Middle Aged
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Mutation*
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Piperazines / therapeutic use
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Protein Kinase Inhibitors / therapeutic use
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Pyridines / therapeutic use
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Skin Neoplasms / drug therapy
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Skin Neoplasms / genetics
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Skin Neoplasms / pathology
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Sweat Gland Neoplasms / drug therapy
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Sweat Gland Neoplasms / genetics
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Sweat Gland Neoplasms / pathology
Substances
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Cyclin-Dependent Kinase Inhibitor p16
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CDKN2A protein, human
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Cyclin-Dependent Kinase 4
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Protein Kinase Inhibitors
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Cyclin-Dependent Kinase 6
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palbociclib
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Pyridines
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Piperazines