Development of clinical and laboratory biomarkers in an international cohort of 428 children with lupus nephritis

Pediatr Nephrol. 2024 Oct;39(10):2959-2968. doi: 10.1007/s00467-024-06405-6. Epub 2024 May 28.

Abstract

Background: Lupus nephritis (LN) is a very severe manifestation of lupus. There is no consensus on which treatment goals should be achieved to protect kidney function in children with LN.

Methods: We retrospectively analyzed trends of commonly used laboratory biomarkers of 428 patients (≤ 18 years old) with biopsy-proven LN class ≥ III. We compared data of patients who developed stable kidney remission from 6 to 24 months with those who did not.

Results: Twenty-five percent of patients maintained kidney stable remission while 75% did not. More patients with stable kidney remission showed normal hemoglobin and erythrocyte sedimentation rate from 6 to 24 months compared to the group without stable kidney remission. eGFR ≥ 90 ml/min/1.73m2 at onset predicted the development of stable kidney remission (93.8%) compared to 64.7% in those without stable remission (P < 0.00001). At diagnosis, 5.9% and 20.2% of the patients showed no proteinuria in the group with and without stable kidney remission, respectively (P = 0.0001). dsDNA antibodies decreased from onset of treatment mainly during the first 3 months in all groups, but more than 50% of all patients in both groups never normalized after 6 months. Complement C3 and C4 increased mainly in the first 3 months in all patients without any significant difference.

Conclusions: Normal eGFR and the absence of proteinuria at onset were predictors of stable kidney remission. Significantly more children showed normal levels of Hb and erythrocyte sedimentation rate (ESR) from 6 to 24 months in the group with stable kidney remission.

Keywords: Biomarkers; Lupus nephritis; Pediatric; Proteinuria; Remission; eGFR.

Publication types

  • Multicenter Study

MeSH terms

  • Adolescent
  • Antibodies, Antinuclear / blood
  • Biomarkers* / blood
  • Blood Sedimentation
  • Child
  • Child, Preschool
  • Complement C3 / analysis
  • Complement C3 / metabolism
  • Complement C4 / analysis
  • Complement C4 / metabolism
  • Female
  • Glomerular Filtration Rate*
  • Humans
  • Kidney / pathology
  • Kidney / physiopathology
  • Lupus Nephritis* / blood
  • Lupus Nephritis* / diagnosis
  • Male
  • Proteinuria / blood
  • Proteinuria / diagnosis
  • Proteinuria / etiology
  • Proteinuria / urine
  • Remission Induction
  • Retrospective Studies

Substances

  • Biomarkers
  • Complement C3
  • Antibodies, Antinuclear
  • Complement C4