Introduction: We report the case of an 18-year-old female with recurrent syncope that was discovered to have congenital long QT syndrome (LQTS) and episodes of a transiently short QT interval after spontaneous termination of polymorphic ventricular tachycardia.
Methods & results: A cardiac event monitor revealed a long QT interval and initiation of polymorphic ventricular tachycardia by a premature ventricular complex on the preceding T-wave. After 1 minute of ventricular fibrillation, her arrhythmia spontaneously terminated with evidence of a short QT interval.
Conclusions: A transient, potentially artificial, short QT interval following Torsades de Pointes can occur in patients with LQTS.
Keywords: catheter ablation-ventricular tachycardia; electrophysiology-cardiac arrest/sudden death; electrophysiology-long QT syndrome; noninvasive techniques-Holter/event recorders; ventricular tachycardia/fibrillation.
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