A Gastroenterologist's Guide to Care Transitions in Cystic Fibrosis from Pediatrics to Adult Care

Int J Mol Sci. 2023 Oct 30;24(21):15766. doi: 10.3390/ijms242115766.

Abstract

Cystic Fibrosis is a chronic disease affecting multiple systems, including the GI tract. Clinical manifestation in patients can start as early as infancy and vary across different age groups. With the advent of new, highly effective modulators, the life expectancy of PwCF has improved significantly. Various GI aspects of CF care, such as nutrition, are linked to an overall improvement in morbidity, lung function and the quality of life of PwCF. The variable clinical presentations and management of GI diseases in pediatrics and adults with CF should be recognized. Therefore, it is necessary to ensure efficient transfer of information between pediatric and adult providers for proper continuity of management and coordination of care at the time of transition. The transition of care is a challenging process for both patients and providers and currently there are no specific tools for GI providers to help ensure a smooth transition. In this review, we aim to highlight the crucial features of GI care at the time of transition and provide a checklist that can assist in ensuring an effective transition and ease the challenges associated with it.

Keywords: cystic fibrosis; gastrointestinal care; highly effective modulators; pancreatic enzyme; pediatrics; transition of care.

Publication types

  • Review

MeSH terms

  • Adult
  • Child
  • Cystic Fibrosis* / complications
  • Cystic Fibrosis* / therapy
  • Gastroenterologists*
  • Gastrointestinal Diseases* / complications
  • Humans
  • Patient Transfer
  • Quality of Life

Grants and funding

This research received no external funding.