Covalent binding of glutathione to hemoglobin. I. Inhibition of hemoglobin S polymerization

J Biol Chem. 1986 Nov 5;261(31):14704-9.

Abstract

Thiol reagents react with cysteine beta 93 of hemoglobin and as a result increase the oxygen affinity of hemoglobin. In the present studies we have used a thiol-disulfide exchange between mixed disulfides of hemoglobin and reduced glutathione to attach intracellular glutathione to hemoglobin and to study its antisickling properties. The rates of production of glutathionyl hemoglobin (G-Hb) depend on the structure of the thiol reagent linked to cysteine beta 93. Up to 25% G-Hb can be produced in normal and sickle red cells because of the high intracellular concentration of reduced glutathione. This high level of G-Hb in normal cells increases the oxygen affinity by about 35% and reduces heme-heme interactions. In sickle cells the increased oxygen affinity is associated with an inhibition of sickling of about 70% at 21 mm Hg. Inhibition of polymerization of deoxy HbS is also due to a direct inhibition of intermolecular contacts in the fibers as demonstrated by the increased solubility and the increased delay time of G-HbS compared to deoxy HbS.

Publication types

  • Comparative Study
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Binding Sites
  • Cysteine*
  • Dithiothreitol / pharmacology
  • Glutathione / blood*
  • Hemoglobin, Sickle / metabolism*
  • Hemoglobins / metabolism*
  • Humans
  • Kinetics
  • Macromolecular Substances
  • Protein Binding

Substances

  • Hemoglobin, Sickle
  • Hemoglobins
  • Macromolecular Substances
  • Glutathione
  • Cysteine
  • Dithiothreitol