Interaction of hemoglobin Siriraj with hemoglobin S: a mild sickle cell syndrome

Hemoglobin. 1986;10(1):21-31. doi: 10.3109/03630268609072468.

Abstract

Hb Siriraj is a beta chain variant in which beta 7 (A4) Glu is replaced by a lysine. It has been encountered in association with Hb S in a black man from Martinique. Some properties of Hb Siriraj are compared, particularly, with Hb C [alpha 2 beta 26(A3)Glu----Lys], and a study of its in vitro interaction with Hb S is discussed.

Publication types

  • Case Reports
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Amino Acid Sequence
  • Anemia, Sickle Cell / blood*
  • Genetic Carrier Screening
  • Genetic Variation
  • Hemoglobin A / metabolism
  • Hemoglobin, Sickle / metabolism*
  • Hemoglobins, Abnormal / genetics
  • Hemoglobins, Abnormal / metabolism*
  • Hemolysis
  • Humans
  • Kinetics
  • Male
  • Middle Aged
  • Syndrome

Substances

  • Hemoglobin, Sickle
  • Hemoglobins, Abnormal
  • Hemoglobin A
  • hemoglobin Siriraj