A Proteomic Survey of the Cystic Fibrosis Transmembrane Conductance Regulator Surfaceome

Int J Mol Sci. 2023 Jul 14;24(14):11457. doi: 10.3390/ijms241411457.

Abstract

The aim of this review article is to collate recent contributions of proteomic studies to cystic fibrosis transmembrane conductance regulator (CFTR) biology. We summarize advances from these studies and create an accessible resource for future CFTR proteomic efforts. We focus our attention on the CFTR interaction network at the cell surface, thus generating a CFTR 'surfaceome'. We review the main findings about CFTR interactions and highlight several functional categories amongst these that could lead to the discovery of potential biomarkers and drug targets for CF.

Keywords: BioID; CFTR interactions; CFTR modulators; PDZ domain; clathrin-mediated endocytosis; cystic fibrosis; interactome; peripheral quality control; surfaceome.

Publication types

  • Review

MeSH terms

  • Cell Membrane* / physiology
  • Cystic Fibrosis Transmembrane Conductance Regulator* / genetics
  • Cystic Fibrosis Transmembrane Conductance Regulator* / metabolism
  • Cystic Fibrosis* / genetics
  • Cystic Fibrosis* / metabolism
  • Humans
  • Ion Transport
  • Mutation
  • Proteomics*
  • Signal Transduction

Substances

  • CFTR protein, human
  • Cystic Fibrosis Transmembrane Conductance Regulator