[Aggressive multifocal extensive cutaneous epithelioid haemagioendothelioma. A case report]

Rev Esp Patol. 2022 Oct-Dec;55(4):254-258. doi: 10.1016/j.patol.2021.03.004. Epub 2021 May 24.
[Article in Spanish]

Abstract

Epithelioid haemangioendothelioma is a rare vascular tumor, first described in 1975 by Dail and Liebow as a bronchioloalveolar carcinoma. Although it usually behaves like a low-grade neoplasm, cases have been reported in which the tumor shows a high grade of malignancy, spreading rapidly throughout the body. We present the case of a 41-year-old man with dermatosis in the left thigh with rapid extension to the abdomen; the initial differential diagnoses were metastatic carcinoma versus lymphoma. When the histopathology was re-examined, a diagnosis of skin epithelioid hemangioendothelioma was confirmed and treatment with radiotherapy was initiated. This tumour rarely affects the skin; there are only a few previously reported cases.

Keywords: Epithelioid haemangioendothelioma; Hemangioendotelioma epitelioide; Neoplasias de piel; Skin neoplasms; Tumores vasculares; Vascular tumors.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Child
  • Diagnosis, Differential
  • Hemangioendothelioma* / diagnosis
  • Hemangioendothelioma, Epithelioid* / diagnosis
  • Humans
  • Male
  • Skin Neoplasms*