Genetic disorders of collagen

J Med Genet. 1987 Jan;24(1):2-8. doi: 10.1136/jmg.24.1.2.

Abstract

Osteogenesis imperfecta, Ehlers-Danlos syndrome, and Marfan syndrome form a group of genetic disorders of connective tissue. These disorders exhibit remarkable clinical heterogeneity which reflects their underlying biochemical and molecular differences. Defects in collagen types I and III have been found in all three syndromes.

Publication types

  • Research Support, Non-U.S. Gov't
  • Research Support, U.S. Gov't, P.H.S.
  • Review

MeSH terms

  • Collagen / genetics*
  • Collagen Diseases / genetics*
  • Ehlers-Danlos Syndrome / genetics
  • Ehlers-Danlos Syndrome / physiopathology
  • Genes
  • Humans
  • Marfan Syndrome / genetics
  • Marfan Syndrome / physiopathology
  • Osteogenesis Imperfecta / genetics
  • Osteogenesis Imperfecta / physiopathology

Substances

  • Collagen