Background: A complex and rare form of double outlet right ventricle needs careful attention when choosing the optimal strategy for repair.
Aim of the study: To point out retrospectively what could have been done differently in our unique patient.
Methods: Primary repair was arranged in a neonate with double outlet right ventricle (of a non-committed ventricular septal defect type and lack of the outlet septum between the semilunar valves) with right aortic arch and dextro-malposition of great arteries.
Results: We managed to achieve intraventricular rerouting via a right ventricular incision concomitantly with the arterial switch maneuver. The patient is doing well with an excellent hemodynamic status.
Conclusions: We considered that the radical approach we chose appeared to be sensible in this particular patient, although some other options could have been available.
Keywords: DORV with noncommitted and doubly-committed VSD; arterial switch in right aortic arch; primary repair of DORV in neonates.
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