Keratosis pilaris in collagen type VI-related disorders

Pediatr Dermatol. 2022 Jan;39(1):133-134. doi: 10.1111/pde.14883. Epub 2022 Jan 5.

Abstract

Keratosis pilaris is a common skin condition associated with a number of syndromes, including collagen type VI-related disorders. Our patient, recently diagnosed with Ullrich congenital muscular dystrophy, presented with severe keratosis pilaris, hypotonia, and velvety skin on the palms and soles. We present this case to highlight the importance of including cutaneous findings, such as keratosis pilaris, to aid in the diagnosis when evaluating patients with syndromic features.

Keywords: Ullrich congenital muscular dystrophy; keratosis pilaris.

MeSH terms

  • Abnormalities, Multiple* / diagnosis
  • Collagen Type VI
  • Darier Disease* / diagnosis
  • Eyebrows / abnormalities
  • Humans

Substances

  • Collagen Type VI

Supplementary concepts

  • Burnett Schwartz Berberian syndrome