Outcomes after lung transplantation among Chinese patients with connective tissue disease-associated interstitial lung disease and pulmonary hypertension: a retrospective cohort study

Clin Exp Rheumatol. 2022 Sep;40(9):1666-1673. doi: 10.55563/clinexprheumatol/hld9sf. Epub 2021 Nov 3.

Abstract

Objectives: The present study aimed to compare the post-lung transplant survival and complications of connective tissue disease (CTD)-related interstitial lung disease (ILD) and/or pulmonary arterial hypertension with idiopathic pulmonary fibrosis (IPF).

Methods: The clinical data of patients with CTD-ILD or IPF who received lung transplantation between 2015 and 2020 were retrospectively reviewed. Cumulative survival rates after transplantation were estimated using the Kaplan-Meier method.

Results: The study included 31 patients with confirmed CTD-ILD and 98 with IPF. Patients with CTD-ILD were significantly younger (53.2 ± 13.7 vs. 62.3 ± 7.2 years, p=0.001) and more likely female (61.3% vs. 7.1%, p<0.001) than patients with IPF. No significant difference was noticed in the 1-year and 5-year survival rates between CTD-ILD and IPF patients (1-year, 73.2% vs 71.4%, p=0.76; 5-year, 69.1% vs. 39.5%, p=0.21). The incidence of primary graft dysfunction was significantly higher in CTD-ILD patients (90.3% vs. 70.4%, p=0.03), while there was no significant difference in primary graft dysfunction-related mortality (6.5% vs. 6.1%, p=0.95) between the two groups.

Conclusions: There was no significant difference in post-lung transplant survival and complications between CTD-ILD and IPF.

MeSH terms

  • China / epidemiology
  • Connective Tissue Diseases*
  • Female
  • Humans
  • Hypertension, Pulmonary* / complications
  • Hypertension, Pulmonary* / surgery
  • Idiopathic Pulmonary Fibrosis* / complications
  • Idiopathic Pulmonary Fibrosis* / surgery
  • Lung Diseases, Interstitial* / complications
  • Lung Diseases, Interstitial* / surgery
  • Lung Transplantation* / adverse effects
  • Primary Graft Dysfunction* / complications
  • Retrospective Studies
  • Tomography, X-Ray Computed / methods