Ciprofloxacin accelerates aortic enlargement and promotes dissection and rupture in Marfan mice

J Thorac Cardiovasc Surg. 2022 Mar;163(3):e215-e226. doi: 10.1016/j.jtcvs.2020.09.069. Epub 2020 Sep 22.

Abstract

Objective: Aortic aneurysm and dissection are major life-threatening complications of Marfan syndrome. Avoiding factors that promote aortic damage is critical in managing the care of these patients. Findings from clinical and animal studies raise concerns regarding fluoroquinolone use in patients at risk for aortic aneurysm and dissection. Therefore, we examined the effects of ciprofloxacin on aortic aneurysm and dissection development in Marfan mice.

Methods: Eight-week-old Marfan mice (Fbn1C1041G/+) were given ciprofloxacin (100 mg/kg/d; n = 51) or vehicle (n = 59) for 4 weeks. Mice were monitored for 16 weeks. Aortic diameters were measured by using ultrasonography, and aortic structure was examined by using histopathologic and immunostaining analyses.

Results: Vehicle-treated Fbn1C1041G/+ mice showed progressive aortic enlargement, with aortic rupture occurring in 5% of these mice. Compared with vehicle-treated Fbn1C1041G/+ mice, ciprofloxacin-treated Fbn1C1041G/+ mice showed accelerated aortic enlargement (P = .01) and increased incidences of aortic dissection (25% vs 47%, P = .03) and rupture (5% vs 25%, P = .005). Furthermore, ciprofloxacin-treated Fbn1C1041G/+ mice had higher levels of elastic fiber fragmentation, matrix metalloproteinase expression, and apoptosis than did vehicle-treated Fbn1C1041G/+ mice.

Conclusions: Ciprofloxacin accelerates aortic root enlargement and increases the incidence of aortic dissection and rupture in Marfan mice, partially by suppressing lysyl oxidase expression and further compromising the inherited defect in aortic elastic fibers. Our findings substantiate that ciprofloxacin should be avoided in patients with Marfan syndrome.

Keywords: Marfan syndrome; aortic disease; ciprofloxacin.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Animals
  • Anti-Bacterial Agents / toxicity*
  • Aorta / drug effects*
  • Aorta / metabolism
  • Aorta / ultrastructure
  • Aortic Aneurysm / chemically induced*
  • Aortic Aneurysm / genetics
  • Aortic Aneurysm / metabolism
  • Aortic Aneurysm / pathology
  • Aortic Dissection / chemically induced*
  • Aortic Dissection / genetics
  • Aortic Dissection / metabolism
  • Aortic Dissection / pathology
  • Aortic Rupture / chemically induced*
  • Aortic Rupture / genetics
  • Aortic Rupture / metabolism
  • Aortic Rupture / pathology
  • Apoptosis / drug effects
  • Ciprofloxacin / toxicity*
  • Dilatation, Pathologic
  • Disease Progression
  • Elastic Tissue / drug effects
  • Elastic Tissue / metabolism
  • Elastic Tissue / ultrastructure
  • Extracellular Matrix Proteins / metabolism
  • Female
  • Fibrillin-1 / genetics*
  • Genetic Predisposition to Disease
  • Male
  • Matrix Metalloproteinases / metabolism
  • Mice
  • Mice, Knockout
  • Phenotype
  • Protein-Lysine 6-Oxidase / metabolism
  • Vascular Remodeling / drug effects*

Substances

  • Anti-Bacterial Agents
  • Extracellular Matrix Proteins
  • Fbn1 protein, mouse
  • Fibrillin-1
  • Lox protein, mouse
  • Ciprofloxacin
  • Protein-Lysine 6-Oxidase
  • Matrix Metalloproteinases