Background: Epidermolysis bullosa is an inherited disease that causes bleeding blisters on the skin tissues and mucosal membranes. This study reports a case of epidermolysis bullosa with clinical manifestations of sepsis and pneumonia.
Case report: A 17-month-old female with epidermolysis bullosa presented with clinical manifestations of sepsis and pneumonia, including increased body temperature, anorexia, and wheezing. Blood test results included the following: white blood cell (WBC) count, 24,000/μl; hemoglobin level, 7.9 mg/dl; erythrocyte sedimentation rate (ESR), 99 mm/h; and C-reactive protein level, +2. The patient was given ceftriaxone, vancomycin, hydrocortisone, and acetaminophen. The patient's fever resolved on the third day of hospitalization, and the ESR and WBC count reached 25 mm/h and 9900/μl, respectively.
Conclusions: According to the report, it is recommended to consider an increase in body temperature, WBC count, and ESR, and perform the required attempts in patients with epidermolysis bullosa.
Keywords: Epidermolysis bullosa; Sepsis; Treatment.
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