Pseudopolymorphic Wide Complex Tachycardia in a Child With Long QT Syndrome

Marina Cerrone; Silvia Magnani; Linda Borneman; Frank Cecchin; Reina Tan; Steven J Fowler; Larry Chinitz; Lior Jankelson

doi:10.1016/j.jaccas.2020.02.011

Pseudopolymorphic Wide Complex Tachycardia in a Child With Long QT Syndrome

JACC Case Rep. 2020 Apr 15;2(4):591-594. doi: 10.1016/j.jaccas.2020.02.011. eCollection 2020 Apr.

Authors

Marina Cerrone¹, Silvia Magnani¹, Linda Borneman¹, Frank Cecchin², Reina Tan², Steven J Fowler^{1

3}, Larry Chinitz¹, Lior Jankelson¹

Affiliations

¹ Heart Rhythm Program and Inherited Arrhythmias Clinic, Leon H Charney Division of Cardiology, New York University School of Medicine, New York, New York.
² Division of Pediatric Cardiology, Department of Pediatrics, New York University School of Medicine, New York, New York.
³ Cardiac Electrophysiology, Community Hospital of Monterey Peninsula, Monterey, California.

Abstract

Implantable loop recorders (ILRs) can be a valuable tool in monitoring patients with inherited arrhythmia. This paper reports on a family with long QT syndrome (type 2 [LQT2]) in which a pseudopolymorphic wide complex tachycardia detected by ILR was ultimately diagnosed as a supraventricular aberrant rhythm, facilitated by noncompliance with beta-blocker therapy. (Level of Difficulty: Intermediate.).

Keywords: EPS, electrophysiology study; ICD, implantable cardioverter defibrillator; ILR, implantable loop recorder; LBBB, left bundle branch block; LQTS, long QT syndrome; QTc, corrected QT interval; SCD, sudden cardiac death; SVT, supraventricular tachycardia; VT, ventricular tachycardia; implantable loop recorder; inherited arrhythmia; long QT syndrome; sudden cardiac death; wide complex tachycardia.

Publication types

Case Reports