Auto-destruction of the thyroid gland and coexisting glutamic acid decarboxylase mediated neurological disease in an adolescent: an unusual presentation of autoimmunity

J Pediatr Endocrinol Metab. 2021 Jun 24;34(10):1329-1333. doi: 10.1515/jpem-2020-0697. Print 2021 Oct 26.

Abstract

Objectives: Hashimoto's thyroiditis (HT) is characterized by lymphocytic thyroid infiltration. Gradual thyroid failure can occur due to thyroid cell apoptosis. Rarely neurological autoimmunity due to glutamic acid decarboxylase (GAD) antigen can co exist with HT.

Case presentation: A seven-year-old male presented with tiredness, weight loss, frequent falls, tachycardia, firm thyromegaly, and abnormal gait. Biochemical markers and thyroid ultrasound (TUS) showed autoimmune hyperthyroidism. Methimazole (MMI) was started and continued for 2.2 years. MRI brain was normal and neurological symptoms resolved. At nine years, he became hypothyroid and levothyroxine (LT4) was started. Serial TUS showed progressive thyroid atrophy. At 14.8 years, he developed epilepsy and fourth cranial nerve palsy, and diagnosed with GAD-65 central nervous system disease. At 15.3 years, TUS showed complete atrophy of right lobe with involuting left lobe volume.

Conclusions: This is an unusual form of atrophic thyroiditis (AT) with coexisting neurological autoimmunity. GAD-65 CNS autoimmunity should be considered in children with AT presenting with neurological signs.

Keywords: GAD mediated CNS disease; apoptosis; autoimmunity; thyroid.

Publication types

  • Case Reports

MeSH terms

  • Adolescent
  • Atrophy / complications
  • Atrophy / diagnosis
  • Autoimmune Diseases / diagnosis
  • Autoimmune Diseases / etiology
  • Autoimmune Diseases of the Nervous System / diagnosis*
  • Autoimmune Diseases of the Nervous System / etiology
  • Child
  • Diagnosis, Differential
  • Glutamate Decarboxylase / immunology*
  • Humans
  • Male
  • Thyroid Gland / diagnostic imaging
  • Thyroid Gland / immunology
  • Thyroid Gland / pathology*
  • Thyroiditis, Autoimmune / complications
  • Thyroiditis, Autoimmune / diagnosis*
  • Thyroiditis, Autoimmune / pathology
  • United States

Substances

  • Glutamate Decarboxylase