A rare case of retroperitoneal teratoma with obstructed hemivagina and ipsilateral renal anomaly (OHVIRA) syndrome

BMJ Case Rep. 2021 May 19;14(5):e243302. doi: 10.1136/bcr-2021-243302.

Abstract

A 9-month-old girl presented with progressive abdominal distension. Imaging revealed a huge cystic mass in the left retroperitoneum with solid components. The right kidney was absent and hydrometrocolpos was found. Tumour drainage and complete surgical excision were performed. A bulge in the right side of the uterus, suggestive of a uterine anomaly, was seen on laparoscopic observation. Pathology was consistent with teratoma with a small portion of immature neural tissue. The patient was discharged in good condition and was advised regular follow-up.

Keywords: congenital disorders; paediatric oncology.

Publication types

  • Case Reports

MeSH terms

  • Female
  • Humans
  • Infant
  • Kidney / diagnostic imaging
  • Kidney / surgery
  • Kidney Diseases*
  • Teratoma* / complications
  • Teratoma* / diagnostic imaging
  • Teratoma* / surgery
  • Urogenital Abnormalities*
  • Uterus
  • Vagina