Enhancing cyst-like lesions of the white matter in tuberous sclerosis complex: a novel neuroradiological finding

Neuroradiology. 2021 Jun;63(6):971-974. doi: 10.1007/s00234-021-02647-5. Epub 2021 Jan 22.

Abstract

Tuberous sclerosis complex (TSC) is an autosomal dominant condition clinically presenting with heterogenous clinical features. Multiple neuroradiological manifestations have been associated with TSC, such as tubers, radial migration lines, subependymal nodules, subependymal giant cell astrocytomas, and cyst-like lesions of the white matter (CLLWMs). The latter have been described as non-enhancing well-defined cysts whose pathogenesis is still unknown. We describe 2 TSC patients with CLLWM showing contrast enhancement after Gadolinium injection, a previously unreported entity.

Keywords: Magnetic resonance imaging; Pediatric neuroradiology; Phakomatosis; Tuberous sclerosis complex.

MeSH terms

  • Astrocytoma*
  • Brain Neoplasms*
  • Cysts*
  • Humans
  • Tuberous Sclerosis* / complications
  • Tuberous Sclerosis* / diagnostic imaging
  • White Matter*