Disseminated cryptococcosis and anti-granulocyte-macrophage colony-stimulating factor autoantibodies: An underappreciated association

Mycoses. 2021 Jun;64(6):576-582. doi: 10.1111/myc.13247. Epub 2021 Feb 5.

Abstract

The development of disseminated cryptococcosis has historically occurred in patients living with advanced human immunodeficiency virus or other immunosuppressive conditions affecting T-cell function. Recently, patients with anti-cytokine neutralising autoantibodies have been recognised to be at risk for disseminated infections by opportunistic intracellular pathogens, including Cryptococcus species. Herein, we present a previously healthy 26-year-old man who was evaluated with disseminated cryptococcosis involving the bone, lung, mediastinum and brain. The patient's serum cryptococcal antigen titres were >1:1,100,000, and evaluation for an underlying immunodeficiency revealed high titres for anti-granulocyte-macrophage colony-stimulating factor (GM-CSF) autoantibodies. We also review the literature of all published cases of disseminated cryptococcosis associated with the presence of anti-GM-CSF autoantibodies. Clinicians should have a heightened awareness of anti-cytokine autoantibodies in patients without a known immunodeficiency and development disseminated infections by opportunistic intracellular pathogens.

Keywords: Cryptococcus; autoantibodies; cytokines; fungus; immunodeficiency; meningitis.

Publication types

  • Case Reports
  • Review

MeSH terms

  • AIDS-Related Opportunistic Infections / complications
  • Adult
  • Autoantibodies / blood
  • Autoantibodies / immunology*
  • Bone and Bones / microbiology
  • Bone and Bones / pathology
  • Cryptococcosis* / immunology
  • Cryptococcosis* / pathology
  • Cryptococcus / immunology*
  • Cytokines / immunology
  • Granulocyte-Macrophage Colony-Stimulating Factor / immunology*
  • Humans
  • Immunosuppression Therapy
  • Invasive Fungal Infections / immunology
  • Invasive Fungal Infections / pathology
  • Lung / microbiology
  • Lung / pathology
  • Male
  • Meningitis, Cryptococcal / diagnosis
  • Meningitis, Cryptococcal / pathology

Substances

  • Autoantibodies
  • Cytokines
  • Granulocyte-Macrophage Colony-Stimulating Factor