Factor XIII (FXIII) deficiency is a rare inherited coagulopathy. Standard perioperative management in those with FXIII deficiency requiring surgical procedures has not been elucidated. Herein, we report the case of a patient with FXIII deficiency who successfully underwent transurethral lithotripsy. Recombinant FXIII was used effectively in perioperative management and safely without any bleeding complications. This is the first report of a patient with FXIII deficiency in the field of urology.
Keywords: Bleeding disorders; Calculus; Congenital coagulation factor XIII deficiency; Factor XIII, (FXIII); Transurethral lithotripsy; computed tomography, (CT); transurethral lithotripsy, (TUL).
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