A case of severe aortic stenosis caused by unicuspid unicommissural aortic valve

Junya Tanabe; Hirotomo Sato; Akihiro Endo; Hiroyuki Yoshitomi; Koji Shimizu; Teiji Oda; Kazuaki Tanabe

doi:10.1016/j.jccase.2020.05.015

A case of severe aortic stenosis caused by unicuspid unicommissural aortic valve

J Cardiol Cases. 2020 Jun 11;22(4):170-173. doi: 10.1016/j.jccase.2020.05.015. eCollection 2020 Oct.

Authors

Junya Tanabe¹, Hirotomo Sato¹, Akihiro Endo¹, Hiroyuki Yoshitomi¹, Koji Shimizu², Teiji Oda², Kazuaki Tanabe¹

Affiliations

¹ Division of Cardiology, Shimane University, Faculty of Medicine, Izumo, Japan.
² Division of Cardiovascular Surgery, Shimane University, Faculty of Medicine, Izumo, Japan.

Abstract

Unicuspid aortic valve (UAV) is an extremely rare congenital malformation that frequently presents with valvular dysfunction or aortic aneurysm. Here we report the case of a 49-year-old man with severe aortic stenosis caused by UAV requiring the Bentall procedure. Two- and three-dimensional transesophageal echocardiography revealed an eccentric opening in an aortic valve and a lateral attachment to the aorta at the orifice level, suggestive of which is consistent with unicommissural UAV as conﬁrmed by surgical ﬁndings. <Learning objective: We report a rare case of unicuspid aortic valve (UAV) requiring the Bentall procedure. This case demonstrates the utility of two- and three-dimensional transesophageal echocardiography in revealing the morphology of UAV, as conﬁrmed by surgical ﬁndings.>.

Keywords: Aortic aneurysm; Aortic valve stenosis; Intracranial aneurysm; Unicuspid aortic valve.

Publication types

Case Reports