A rare case of pediatric Tolosa-Hunt syndrome

J AAPOS. 2020 Oct;24(5):316-319. doi: 10.1016/j.jaapos.2020.05.009. Epub 2020 Sep 2.

Abstract

Tolosa-Hunt syndrome is a rare disorder characterized by granulomatous inflammation involving the cavernous sinus, superior orbital fissure, and/or orbit with no additional underlying cause. Tolosa-Hunt syndrome most often presents with painful ophthalmoplegia involving one or multiple cranial nerves. Here we report the case of an 8-year-old girl who presented, atypically, without the hallmark finding of pain. This case of pediatric Tolosa-Hunt syndrome is the only reported example to date lacking what is considered its pathognomonic feature and thus brings to light the clinical variability of this already inconspicuous disorder.

Publication types

  • Case Reports

MeSH terms

  • Cavernous Sinus*
  • Child
  • Cranial Nerves
  • Diagnosis, Differential
  • Female
  • Humans
  • Magnetic Resonance Imaging
  • Ophthalmoplegia* / diagnosis
  • Tolosa-Hunt Syndrome* / diagnosis