The expression of platelet-derived growth factor receptor alpha-positive cells in the stenotic tissue of ureteropelvic junction obstruction in children

Clin Nephrol. 2020 Apr;93(4):195-202. doi: 10.5414/CN110009.

Abstract

Aim: By observing the expression and distribution of platelet-derived growth factor receptor α-positive (PDGFRα+) cells in ureteropelvic junction obstruction (UPJO), to explore their role in the pathogenesis of children with congenital hydronephrosis.

Materials and methods: The control group involved specimens of the normal ureter (nephrectomy for tumor; n = 10), and the UPJO group contained specimens of ureteropelvic junction (UPJ) segment excised during pyeloplasty (n = 30). The specimens were investigated using immunofluorescence for the expression and distribution of PDGFRα+ cells in each group by light microscopy with computerized image analysis. Real-time PCR (RT-PCR) was used to study PDGFRα gene expression levels. In addition, small conductance calcium-activated potassium channel 3 (SK3) and closely associated cells consisting of smooth muscle cells (SMCs), interstitial cells of Cajal (ICCs), and nerve fibers were investigated.

Results: PDGFRα+ cells were in close proximity to SMCs, ICCs, and nerve fibers. PDGFRα+ cells expressed SK3 channels, which are found to regulate purinergic inhibitory neurotransmission in SMCs. Regarding the expression of PDGFRα+ cells no significant difference was seen between the two groups, while the expression of SK3 channels in PDGFRα+ cells was significantly decreased in the UPJO group versus the control group.

Conclusion: This study identified the expression of PDGFRα+ cells in the human UPJ. Our results demonstrate the expression of SK3 channels in PDGFRα+ cells was decreased in UPJO, and SK3 channels may be involved in the pathogenesis of UPJO by perturbing the UPJ peristalsis.

MeSH terms

  • Child
  • Child, Preschool
  • Constriction, Pathologic
  • Humans
  • Infant
  • Kidney Pelvis / pathology*
  • Receptor, Platelet-Derived Growth Factor alpha / analysis*
  • Receptor, Platelet-Derived Growth Factor alpha / physiology
  • Small-Conductance Calcium-Activated Potassium Channels / physiology
  • Ureter / pathology*
  • Ureteral Obstruction / etiology*

Substances

  • KCNN3 protein, human
  • Small-Conductance Calcium-Activated Potassium Channels
  • Receptor, Platelet-Derived Growth Factor alpha