Current and Future Idiopathic Pulmonary Fibrosis Therapy

Am J Med Sci. 2019 May;357(5):370-373. doi: 10.1016/j.amjms.2019.02.006. Epub 2019 Feb 11.

Abstract

The last years have led to advances in the therapeutic management of idiopathic pulmonary fibrosis (IPF), mainly through the discovery of new pathological pathways and drugs and better design of clinical trials. The objective of this review is both to describe the current therapies approved for the treatment of IPF and the emerging therapeutic approaches. Currently, nintedanib and pirfenidone are the basis of IPF therapy, based on the results of large randomized clinical trials showing their safety and efficacy in reducing disease progression. Nonetheless, the ideal IPF therapy is still lacking and trials are underway to test new therapeutic targets. The near future could bring to clinicians and patients a combined therapeutic strategy, hitting the disease from several simultaneous pathways and hopefully leading to clinical stabilization or improvement.

Keywords: Clinical trials; Idiopathic pulmonary fibrosis; Nintedanib; Pirfenidone.

Publication types

  • Research Support, Non-U.S. Gov't
  • Review

MeSH terms

  • Anti-Inflammatory Agents / therapeutic use*
  • Disease Progression
  • Humans
  • Idiopathic Pulmonary Fibrosis / therapy*
  • Indoles / therapeutic use*
  • Pyridones / therapeutic use*

Substances

  • Anti-Inflammatory Agents
  • Indoles
  • Pyridones
  • pirfenidone
  • nintedanib