The Small Fatal Choroidal Melanoma Study. A Survey by the European Ophthalmic Oncology Group

Am J Ophthalmol. 2019 Jun:202:100-108. doi: 10.1016/j.ajo.2019.01.031. Epub 2019 Feb 15.

Abstract

Purpose: To determine the size at which choroidal melanomas can metastasize and to report the characteristics of small fatal choroidal melanomas (SFCM).

Design: Retrospective case series.

Methods: Ten ocular oncology services submitted 45 patients with a choroidal melanoma 3 mm or less in thickness and 9 mm or less in largest basal diameter (LBD), when treated, who developed metastases.

Results: Median tumor thickness was 2.4 mm (range, 1.0-3.0 mm) and LBD 7.3 mm (range, 3.0-9.0 mm). Of 14 (31%) tumors that were first observed, 12 grew a median of 0.5 mm (range, 0.1-1.2 mm) in thickness and 1.0 mm (range, 0-3.0 mm) in LBD within a median of 7 months; 3 were initially smaller than 3 mm in LBD. Number of risk factors for growth and metastasis was 0 for 4% of the tumors; 60% were over 2 mm in thickness, 63% had subretinal fluid, 84% caused symptoms, 57% had orange pigment, and 92% were within 3 mm of the disc. Local recurrence occurred in 8 of 31 eyes (26%) treated conservatively. Median metastasis-free survival was 4.5 years (range, 0.8-15.7 years). Kaplan-Meier estimate of metastasis developing was 15% (95% confidence interval [CI], 7-26), 51% (95% CI, 36-64) and 85% (95% CI, 71-92) by 2, 5, and 10 years, respectively. By the time of analysis, 37 patients had died of metastasis after a median of 7 months.

Conclusions: Choroidal melanomas less than 3.0 mm in LBD are highly unlikely to metastasize. Risk factors of an SFCM are similar to those for all choroidal melanomas of similar size.

Publication types

  • Multicenter Study
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adult
  • Aged
  • Aged, 80 and over
  • Choroid / diagnostic imaging*
  • Choroid Neoplasms / diagnosis*
  • Choroid Neoplasms / mortality
  • Choroid Neoplasms / therapy
  • Combined Modality Therapy
  • Europe / epidemiology
  • Female
  • Follow-Up Studies
  • Humans
  • Male
  • Melanoma / diagnosis*
  • Melanoma / mortality
  • Melanoma / therapy
  • Middle Aged
  • Neoplasm Staging*
  • Prognosis
  • Retrospective Studies
  • Risk Factors
  • Surveys and Questionnaires*
  • Survival Rate / trends
  • Ultrasonography
  • Visual Acuity*