Marfan syndrome in a term-pregnant woman with aortic root dilatation between 40 and 45 mm

Abstract

Marfan syndrome is a hereditary connective tissue disorder. The main cause of mortality in these patients is due to cardiovascular complications related to dilation of an aneurysm and dissection of the aortic root, a situation that increases their risk due to the physiological changes that occur during pregnancy, childbirth and puerperium. The case is presented of a pregnant woman with Marfan syndrome and aortic root dilatation of 42mm. The issues are discussed, such as the mode of delivery (vaginal delivery vs. caesarean section) depending on the aortic root diameter or the choice of type of anaesthesia (general vs. neuraxial) in these cases.

Keywords: Anaesthesia; Anestesia; Anestesia obstétrica; Aortic root diameter; Aortic root dilation; Caesarean section; Cesárea; Dilatación raíz aórtica; Diámetro raíz aórtica; Marfan syndrome; Obstetric anaesthesia; Obstetricia; Obstetrics; Síndrome de Marfan.