Abstract
Purpose of review:
This review offers recommendations for monitoring disease status in ocular cicatricial pemphigoid as well therapeutic options including local and systemic therapies.
Recent findings:
A negative biopsy on direct immunofluorescence does not preclude a diagnosis of OCP. If a patient's cicatrization is active and/or progressive, systemic immunosuppression should be commenced.
Summary:
OCP is a chronic systemic autoimmune disease that requires systemic immunosuppression.
MeSH terms
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Autoimmune Diseases / diagnosis*
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Autoimmune Diseases / drug therapy
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Biopsy
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Complement C3 / immunology
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Conjunctival Diseases / diagnosis*
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Conjunctival Diseases / drug therapy
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Epithelial Cells / immunology
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Epithelial Cells / pathology
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Humans
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Immunoglobulin A / immunology
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Immunosuppressive Agents / therapeutic use
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Pemphigoid, Benign Mucous Membrane / diagnosis*
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Pemphigoid, Benign Mucous Membrane / drug therapy
Substances
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Complement C3
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Immunoglobulin A
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Immunosuppressive Agents