Cauda equina syndrome in a patient diagnosed with type 1 Gaucher disease: a rare case

Childs Nerv Syst. 2019 Jan;35(1):191-194. doi: 10.1007/s00381-018-3946-z. Epub 2018 Aug 9.

Abstract

Background: Gaucher disease is a rare hereditary glycolipid storage disease. One of the rare complications is neurodeficits due to vertebral involvement.

Case presentation: An 18-year-old female patient presented to the outpatient clinic with cauda equina syndrome due to sacral involvement of type 1 GD. Bilateral laminectomy via posterior approach without posterior stabilization was performed.

Conclusion: Maximum excision of the mass avoiding destabilization of the spinal column can provide long-term vertebral stability and improvement in neurodeficits.

Keywords: Cauda equina; Gaucher; Sacral mass.

Publication types

  • Case Reports

MeSH terms

  • Adolescent
  • Cauda Equina Syndrome / diagnostic imaging
  • Cauda Equina Syndrome / etiology*
  • Cauda Equina Syndrome / surgery
  • Decompression, Surgical
  • Enzyme Replacement Therapy / methods
  • Female
  • Gaucher Disease / complications*
  • Gaucher Disease / surgery
  • Gaucher Disease / therapy
  • Humans
  • Laminectomy / methods
  • Magnetic Resonance Imaging
  • Neurosurgical Procedures / methods
  • Treatment Outcome