Congenital right bronchial stenosis with high bifurcation: Successful management with side to side tracheobronchial anastomosis

Int J Pediatr Otorhinolaryngol. 2018 Aug:111:180-182. doi: 10.1016/j.ijporl.2018.06.011. Epub 2018 Jun 12.

Abstract

Congenital bronchial stenosis is a rare entity [1,2]. While there are some reports of congenital bronchial anomalies and their repair in the thoracic literature this is first report in the literature of a bronchial take off just below the larynx managed with surgical success. Here we present a case of a former 33-weeker born with a tracheoesophageal fistula, Tetralogy of Fallot, and a high bifurcation of the right mainstem bronchus with a concomitant long segment bronchial stenosis. Preoperative planning included printing 3-D reconstructed models of the airway to analyze various treatment options. At 3 months of age the patient was taken to the operating room for surgical repair of the Tetralogy of Fallot and side-to-side tracheobroncheoplasty. The patient was extubated on postoperative day 3 and was discharged home without need for any ventilatory support.

Keywords: 3D model; Bifurcation; Bronchial; Congenital; Double trachea; Stenosis.

Publication types

  • Case Reports

MeSH terms

  • Abnormalities, Multiple / diagnosis
  • Abnormalities, Multiple / surgery*
  • Anastomosis, Surgical
  • Bronchi / abnormalities
  • Bronchi / surgery*
  • Bronchial Diseases / congenital
  • Bronchial Diseases / diagnosis
  • Bronchial Diseases / surgery*
  • Constriction, Pathologic
  • Humans
  • Infant
  • Male
  • Tetralogy of Fallot / diagnosis
  • Tetralogy of Fallot / surgery
  • Trachea / surgery*
  • Tracheoesophageal Fistula / congenital
  • Tracheoesophageal Fistula / diagnosis
  • Tracheoesophageal Fistula / surgery