A Small Molecule Inhibitor of Plasminogen Activator Inhibitor-1 Reduces Brain Amyloid-β Load and Improves Memory in an Animal Model of Alzheimer's Disease

J Alzheimers Dis. 2018;64(2):447-457. doi: 10.3233/JAD-180241.

Abstract

Alzheimer's disease (AD) is a major cause of dementia in the elderly with no effective treatment. Accumulation of amyloid-β peptide (Aβ) in the brain is a pathological hallmark of AD and is believed to be a central disease-causing and disease-promoting event. In a previous study, we showed that deletion of plasminogen activator inhibitor 1 (PAI-1), a primary inhibitor of tissue type and urokinase type plasminogen activators (tPA and uPA), significantly reduced brain Aβ load in APP/PS1 mice, an animal model of familial AD. In this study, we further show that oral administration of TM5275, a small molecule inhibitor of PAI-1, for a period of 6 weeks, inhibits the activity of PAI-1 and increases the activities of tPA and uPA as well as plasmin, which is associated with a reduction of Aβ load in the hippocampus and cortex and improvement of learning/memory function in APP/PS1 mice. Protein abundance of low density lipoprotein related protein-1 (LRP-1), a multi ligand endocytotic receptor involved in transporting Aβ out of the brain, as well as plasma Aβ42 are increased, whereas the expression and processing of full-length amyloid-β protein precursor is not affected by TM5275 treatment in APP/PS1 mice. In vitro studies further show that PAI-1 increases, whereas TM5275 reduces, Aβ40 level in the culture medium of SHSY5Y-APP neuroblastoma cells. Collectively, our data suggest that TM5275 improves memory function of APP/PS1 mice, probably by reducing brain Aβ accumulation through increasing plasmin-mediated degradation and LRP-1-mediated efflux of Aβ in the brain.

Keywords: Alzheimer’s disease; PAI-1 inhibitor; amyloid-β accumulation; memory.

Publication types

  • Research Support, N.I.H., Extramural

MeSH terms

  • Alzheimer Disease / complications*
  • Alzheimer Disease / genetics
  • Amyloid beta-Peptides / metabolism*
  • Amyloid beta-Protein Precursor / genetics
  • Animals
  • Brain / drug effects*
  • Brain / metabolism
  • Cell Line, Tumor
  • Disease Models, Animal
  • Exploratory Behavior / drug effects
  • Female
  • Gene Expression Regulation / drug effects
  • Gene Expression Regulation / genetics
  • Male
  • Maze Learning / drug effects
  • Memory Disorders* / drug therapy
  • Memory Disorders* / etiology
  • Memory Disorders* / pathology
  • Mice
  • Mice, Transgenic
  • Mutation / genetics
  • Neuroblastoma / pathology
  • Piperazines / therapeutic use*
  • Plasminogen Activator Inhibitor 1 / metabolism
  • Presenilin-1 / genetics
  • Urokinase-Type Plasminogen Activator / metabolism
  • para-Aminobenzoates / therapeutic use*

Substances

  • 5-chloro-2-(((2-(4-(diphenylmethyl)piperazin-1-yl)-2-oxoethoxy)acetyl)amino)benzoate
  • Amyloid beta-Peptides
  • Amyloid beta-Protein Precursor
  • PSEN1 protein, human
  • Piperazines
  • Plasminogen Activator Inhibitor 1
  • Presenilin-1
  • para-Aminobenzoates
  • Urokinase-Type Plasminogen Activator