[Analysis of a neonate with bullous congenital ichthyosiform erythroderma with next generation sequencing]

Zhonghua Yi Xue Yi Chuan Xue Za Zhi. 2018 Jun 10;35(3):434-436. doi: 10.3760/cma.j.issn.1003-9406.2018.03.029.
[Article in Chinese]

Abstract

Objective: To explore the genetic cause and clinical features of a neonate with bullous congenital ichthyosiform erythroderma.

Methods: The patient was examined thoroughly. Following the extraction of genomic DNA, next generation sequencing was performed to analyze the genetic cause.

Results: The patient manifested generalized erythema, blistering, and extensive exfoliation of the skin. A heterozygous missence 482T>G mutation was found in the first exon of KRT10 gene, which led to a p.L161W alteration in its protein product.

Conclusion: The de novo mutation of the KRT10 gene probably underlies the disease in the child.

Publication types

  • Case Reports

MeSH terms

  • Base Sequence
  • Exons
  • Heterozygote
  • High-Throughput Nucleotide Sequencing
  • Humans
  • Hyperkeratosis, Epidermolytic / genetics*
  • Infant, Newborn
  • Keratin-10 / genetics
  • Male
  • Mutation

Substances

  • KRT10 protein, human
  • Keratin-10