Recurrent pulmonary embolism associated with deep venous thrombosis diagnosed as protein s deficiency owing to a novel mutation in PROS1: A case report

Medicine (Baltimore). 2018 May;97(19):e0714. doi: 10.1097/MD.0000000000010714.

Abstract

Rationale: Protein S (PS) deficiency that can be inherited or acquired is an independent risk factor for venous thromboembolism (VTE).

Patient concerns: In this report, we present a case of recurrent pulmonary embolism (PE) and deep venous thrombosis (DVT) due to PS deficiency.

Diagnoses: A 32-year-old male patient with significant decrease in PS activity was detected by laboratory tests. Genetic examination of the PROS1 gene showed a transition of G to T in exon 14 (c.1792 G>T, p.E598X), which was a paternal inherited heterozygous G1792T substitution in the laminin G-type repeat domain, generating a premature stop codon at Glu598.

Interventions: We considered that the inherited PS deficiency due to a PROS1 gene mutation may associate with recurrent VTE. The patient was suggested to have an extended anticoagulant therapy to avoid a severe VTE event.

Outcomes: The patient was discharged home with continued oral anticoagulants and was still seen in clinic for follow-up.

Lessons: It is necessary for the young patient with recurrent idiopathic thrombosis to perform an inherited PS deficiency test and receive anticoagulant therapy for an extended period.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Blood Proteins / genetics*
  • Humans
  • Male
  • Mutation*
  • Protein S
  • Protein S Deficiency / complications
  • Protein S Deficiency / diagnosis*
  • Protein S Deficiency / genetics*
  • Pulmonary Embolism / etiology*
  • Recurrence
  • Venous Thrombosis / etiology*

Substances

  • Blood Proteins
  • PROS1 protein, human
  • Protein S