Successful multi-target therapy including rituximab and mycophenolate mofetil in anti-melanoma differentiation-associated gene 5 antibody-positive rapidly progressive interstitial lung disease with clinically amyopathic dermatomyositis

Int J Rheum Dis. 2017 Dec;20(12):2182-2185. doi: 10.1111/1756-185X.13136. Epub 2017 Jul 27.
No abstract available

Publication types

  • Case Reports
  • Letter

MeSH terms

  • Autoantibodies / blood
  • Autoantibodies / immunology*
  • Dermatomyositis / diagnosis
  • Dermatomyositis / drug therapy*
  • Dermatomyositis / immunology
  • Drug Therapy, Combination
  • Female
  • Hemoperfusion / methods
  • Humans
  • Immunoglobulins, Intravenous / therapeutic use
  • Immunosuppressive Agents / therapeutic use*
  • Interferon-Induced Helicase, IFIH1 / immunology*
  • Lung Diseases, Interstitial / diagnosis
  • Lung Diseases, Interstitial / drug therapy*
  • Lung Diseases, Interstitial / immunology
  • Middle Aged
  • Mycophenolic Acid / therapeutic use*
  • Remission Induction
  • Rituximab / therapeutic use*
  • Tomography, X-Ray Computed
  • Treatment Outcome

Substances

  • Autoantibodies
  • Immunoglobulins, Intravenous
  • Immunosuppressive Agents
  • Rituximab
  • IFIH1 protein, human
  • Interferon-Induced Helicase, IFIH1
  • Mycophenolic Acid

Supplementary concepts

  • Amyopathic dermatomyositis