Duane syndrome with prominent oculo-auricular phenomenon

J AAPOS. 2017 Apr;21(2):165-167. doi: 10.1016/j.jaapos.2016.09.017. Epub 2016 Dec 10.

Abstract

Duane syndrome is a congenital cranial dysinnervation disorder involving absent or anomalous innervation of the lateral and medial rectus muscles that is sometimes associated with other manifestations of dysinnervation. We describe a patient with right esotropic Duane syndrome with a long-standing retroauricular tugging sensation in right gaze who was noted to have prominent ipsilateral oculo-auricular phenomenon, representing either abnormal enhancement of existing innervation or an uncommon dysinnervation. After successful strabismus surgery the tugging sensation improved but the phenomenon could still be elicited.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Duane Retraction Syndrome / diagnosis*
  • Duane Retraction Syndrome / physiopathology
  • Duane Retraction Syndrome / surgery
  • Eye Movements / physiology*
  • Humans
  • Male
  • Oculomotor Muscles / physiopathology
  • Oculomotor Muscles / surgery*
  • Ophthalmologic Surgical Procedures / methods*
  • Vision, Binocular / physiology*