Anti-N-methyl-D-aspartate receptor encephalitis with an imaging-invisible ovarian teratoma: a case report

J Med Case Rep. 2016 Oct 24;10(1):296. doi: 10.1186/s13256-016-1067-4.

Abstract

Background: Anti-N-methyl-D-aspartate receptor encephalitis is a recently discovered disease entity of paraneoplastic limbic encephalitis. It largely affects young women and is often associated with an ovarian teratoma. It is a serious yet treatable condition if diagnosed early. Its remedy involves immunotherapy and surgical removal of the teratoma of the ovaries. This case of anti-N-methyl-D-aspartate receptor encephalitis involves an early surgical intervention with bilateral oophorectomy, despite negative imaging evidence of a teratoma.

Case presentation: A 25-year-old white woman with anti-N-methyl-D-aspartate receptor encephalitis presented with behavioral changes and seizures that were confirmed to be secondary to anti-N-methyl-D-aspartate receptor encephalitis. She required an admission to our intensive care unit for ventilator support and received a number of immunological therapies. Multiple imaging investigations showed no evidence of an ovarian teratoma; she had a bilateral oophorectomy 29 days after admission. Ovarian histology confirmed the presence of a teratoma with neuronal cells. A few days after the operation she began to show signs of improvement and, apart from mild short-term memory loss, she returned to normal function.

Conclusions: Our patient is an example of teratoma-associated anti-N-methyl-D-aspartate receptor encephalitis, in which the teratoma was identified only microscopically. Her case highlights that even with negative imaging evidence of a teratoma, ovarian pathology should still be considered and explored.

Keywords: Case report; Encephalitis; NMDA receptor; Oophorectomy; Paraneoplastic; Teratoma.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Anti-N-Methyl-D-Aspartate Receptor Encephalitis / complications*
  • Anti-N-Methyl-D-Aspartate Receptor Encephalitis / diagnosis*
  • Anti-N-Methyl-D-Aspartate Receptor Encephalitis / physiopathology
  • Anti-N-Methyl-D-Aspartate Receptor Encephalitis / therapy
  • Female
  • Humans
  • Immunohistochemistry
  • Immunotherapy
  • Mental Disorders / etiology
  • Ovarian Neoplasms / complications*
  • Ovarian Neoplasms / diagnosis*
  • Ovarian Neoplasms / pathology
  • Ovarian Neoplasms / therapy
  • Ovariectomy
  • Respiration, Artificial
  • Seizures / etiology
  • Teratoma / complications*
  • Teratoma / diagnosis*
  • Teratoma / pathology
  • Teratoma / therapy
  • Treatment Outcome

Supplementary concepts

  • Teratoma, Ovarian