Chronic Recurrent Multifocal Q Fever Osteomyelitis in Children: An Emerging Clinical Challenge

Pediatr Infect Dis J. 2016 Sep;35(9):972-6. doi: 10.1097/INF.0000000000001211.

Abstract

Background: Clinical disease caused by Coxiella burnetii occurs infrequently in children. Chronic Q fever is particularly uncommon and endocarditis is rarely seen. A small number of cases of Q fever osteomyelitis have been described but the pathophysiology is not well understood and optimal treatment is unknown.

Methods: We describe a series of cases of chronic recurrent multifocal Q fever osteomyelitis cases diagnosed in children from a single region in Australia.

Results: Between 2011 and 2014, 9 cases of chronic recurrent multifocal Q fever osteomyelitis were diagnosed based on clinical findings, suggestive serology and detection of C. burnetii DNA by polymerase chain reaction testing of biopsy samples (8/9). All required surgical management; antibiotic and adjuvant therapies did not appear to be consistently effective and 2 cases had clinical resolution in the absence of directed antimicrobial therapy.

Conclusions: Chronic recurrent multifocal osteomyelitis is a rare manifestation of chronic Q fever infection in children. The pathophysiology of this condition is poorly understood, and effective treatment options have not been established.

MeSH terms

  • Anti-Bacterial Agents / therapeutic use
  • Child
  • Child, Preschool
  • Cohort Studies
  • Coxiella burnetii
  • Debridement
  • Female
  • Humans
  • Male
  • Osteomyelitis / diagnosis*
  • Osteomyelitis / therapy*
  • Q Fever / diagnosis*
  • Q Fever / therapy*
  • Treatment Outcome

Substances

  • Anti-Bacterial Agents

Supplementary concepts

  • Chronic recurrent multifocal osteomyelitis