[Clear cell sarcoma of kidney in children]

Bull Cancer. 2016 Apr;103(4):402-11. doi: 10.1016/j.bulcan.2016.01.017. Epub 2016 Feb 28.
[Article in French]

Abstract

Clear cell sarcoma of the kidney (CCSK) is a rare tumor that is diagnosed most often in children between 2- and 4-years-old of age. Usually, patients with CCSK are treated in international study for intrarenal tumors, preferentially Wilms tumor, according to bad histopronostic group. The purpose of this paper is to review the most important features in 2015 about epidemiology, radiology, anatomopathology and genetic of CCSK, and above all a synthesis about successive treatment strategies with their results. Second most common pediatric renal tumor in children less than 5-years-old, its prognosis has improved dramatically in recent years with the use of anthracyclines.

Keywords: Anthracycline; Children; Clear cell sarcoma of kidney; Enfant; Renal tumor; Sarcomes cellules claires; Tumeurs rénales.

Publication types

  • English Abstract

MeSH terms

  • Anthracyclines / therapeutic use
  • Antineoplastic Agents / adverse effects
  • Antineoplastic Agents / therapeutic use
  • Biopsy / methods
  • Child, Preschool
  • Humans
  • Infant
  • Kidney Neoplasms* / diagnosis
  • Kidney Neoplasms* / epidemiology
  • Kidney Neoplasms* / pathology
  • Kidney Neoplasms* / therapy
  • Neoplasm Recurrence, Local / diagnosis
  • Nephrectomy / adverse effects
  • Radiation Injuries / complications
  • Radiotherapy Dosage
  • Rare Diseases* / diagnosis
  • Rare Diseases* / epidemiology
  • Rare Diseases* / pathology
  • Rare Diseases* / therapy
  • Sarcoma, Clear Cell* / diagnosis
  • Sarcoma, Clear Cell* / epidemiology
  • Sarcoma, Clear Cell* / pathology
  • Sarcoma, Clear Cell* / therapy

Substances

  • Anthracyclines
  • Antineoplastic Agents