External compression of the popliteal artery is probably still underdiagnosed. Young patients with atypical claudication, with isolated popliteal changes, deserve thorough investigation. Subdividing the entrapment syndrome into three subgroups (I-III) highlights the clinically important characteristics of the different types. Delayed diagnosis leads to arterial occlusion with clinical and radiological resemblance to arteriosclerotic occlusive disease. At this stage a medial approach with reversed saphenous vein bypass is recommended. If the artery is still patent, a posterior S-shape approach offers good exposure for arterial decompression, rerouting and possible ancillary measures. In addition to reviewing the literature and outlining the classification criteria and surgical treatment, five cases of our own are presented including two rarities. In one both type I and type III existed simultaneously. In the other the popliteal artery entrapment was combined with cystic adventitial disease.